Clinical cases


Introduction. Angiokeratomas are telangiectatic papules histologically characterised by vascular ectasias of the superfical dermis and covered by a hyperkeratotic epidermis. Circumscribed nevoid angiokeratoma (ACN) is a rare congenital vascular malformation.

Clinical case. We report the case of a 20-year-old patient presenting from birth with multiple clustered hyperkeratotic papules located on the anterior thorax. The dermatological examination identified multiple dark red hyperkeratotic papules, varying in size between 2 and 3 mm, located on top a slightly edematous plaque located on the anterior thorax. Histopatological examination revealed a orthokeratotic epidermis and multiple dilated capillaries in the superficial dermis.

Discussions. ACN was decribed in 1890, being more common in females. It is characterized by multiple smallsized angiokeratomas located on a limb segment, buttocks, neck and trunk. The lesions may follow a linear distribution. The treatment consists of surgical excision, cyotherapy, electrosurgery and lasertherapy.