Summary

Introduction: Linear and whorled nevoid hyper-melanosis (LWNH) is a rare, asymptomatic condition mainly affecting the Blaschko lines.

Case report: We report the case of a 5-year-old female patient who presented with clinically ill-defined brown macules on the trunk and upper limbs. Wood lamp examination highlighted clearly demarcated lesions, while dermoscopy identified hyperpigmented areas arranged in a parallel manner. The diagnosis of LWNH was established, and the patient was reassured of the benign nature of the disease.

Conclusions: LWNH is a benign skin condition that can be associated with systemic comorbidities. Future promising therapeutic options are much-needed additions to this complex disease approach.