Introduction:

Endometriosis is defined by the presence of functional endometrial tissue outside of the uterine cavity; the skin involvement is very rare, and the umbilical one is exceptional.

Clinical case:

A 34 year-old female patient presented to the consultation for the appearance of a brown, firm, painless umbilical nodule that present periodical bleeding related to menstruation. Histopathology revealed glandular structures corresponding to the cutaneous endometriosis.
Surgical excision of the tumor was performed.

Discussion:

Primitive umbilical endometriosis is characterized by a firm nodule, located on the umbilicus.
Histology reveals the appearance of ectopic endometrial tissue. The treatment of choice is surgical consisting of omphalectomy with abdominal-pelvic cavity exploration.