Abstract
Linear IgA bullous dermatosis is a rare autoimmune
disease, characterized by the linear deposition of
immunoglobulin A along the basement membrane and by
the possible presence of serum Ig A auto-antibodies. The
peculiarity of this pathology is given by the variable clinical
aspect and by the resemblance with various dermatological
pathologies such as dermatitis herpetiformis, bullous lupus
erythematosus, bullous pemphigoid. A certain diagnosis is
given by direct immunofluorescence that detects a linear
pattern at basal membrane level.
We report a case of linear IgA bullous dermatosis
atypical in matter of clinical appearance and etiopathogenesis
, with prompt response to dapsone treatment and favourable
evolution.