Endometriosis is defined by the presence of functional endometrial tissue outside of the uterine cavity; the skin involvement is very rare, and the umbilical one is exceptional.
A 34 year-old female patient presented to the consultation for the appearance of a brown, firm, painless umbilical nodule that present periodical bleeding related to menstruation. Histopathology revealed glandular structures corresponding to the cutaneous endometriosis.
Surgical excision of the tumor was performed.
Primitive umbilical endometriosis is characterized by a firm nodule, located on the umbilicus.
Histology reveals the appearance of ectopic endometrial tissue. The treatment of choice is surgical consisting of omphalectomy with abdominal-pelvic cavity exploration.